Should we perform systematic electrophysiological study in Steinert's disease?
نویسنده
چکیده
Myotonic dystrophy type 1 (Steinert's disease) is a multisystem disorder with autosomal dominant inheritance. This disease is associated with the presence of an abnormal expansion of a cytosine thymine-guanine (CTG) trinucleotide repeat on chromosome 19q13.3. Because of rhythmic complications, the place for systematic electrophysiological study (EPS) has to be discussed.
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ورودعنوان ژورنال:
- Journal of Cardiothoracic Surgery
دوره 3 شماره
صفحات -
تاریخ انتشار 2008